LYMPHOMATOID GRANULOMATOSIS AT YOUNG AGE

Abstract
Lymphomatoid granulomatosis(LYG) is more common in male adults and rarely seen in children and adolescents. In this paper, we evaluated the clinical characteristics, laboratory findings, treatment and prognosis of young patients with LYG reported in the English literature. Sixteen young case reports were evaluated in detail. Pulmonary involvement which is almost the rule for adult patients is seen in 75% of the young patients. In some young patient with LYG were detected central nervous system involvement or skin involvement without pulmonary involvement. Hypogammaglobulinemia was found in some cases. Therapy modalities were similar to adults. Prednisolone, cyclophosphamide and vincristine were most common drugs for treatment in this group.Prognosis in young patients were worse than elderly patients.

Key words
Granulomatosis linfomatoidea, niñez

Bibliografía del artículo

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